Mounier-Kuhn syndrome
Mounier-Kuhn syndrome
Definition
Mounier-Kuhn syndrome, also known as idiopathic tracheobronchomegaly, is a congenital disorder characterized by marked dilatation of the trachea and proximal bronchi that leads to impaired airway secretion clearance and recurrent lower respiratory tract infections.
Also known as congenital tracheobronchomegaly, idiopathic tracheobronchomegaly, Mounier-Kuhn syndrome, tracheobronchomegaly — per MONDO
Also identified as
- ICD9 748.3 per MONDO
- MESH D014137 per MONDO
- NCIT C85196 per MONDO
- OMIM 275300 per MONDO
- Orphanet 3347 per MONDO
- SCTID 57451009 per MONDO
- UMLS C0040587 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |